Cutaneous Hemangioendothelioma with Intramammary Node Metastasis: Case Report and Review of Literature
Author(s): Melisa Camaño, Carlos Palacio, Marta Gonda, Clara Delbene, Florencia Rébora, Daniela De Boni.
Epithelioid hemangioendothelioma is a rare malignant vascular neoplasm. The skin presentations often have a delayed diagnosis because of their nonspecific presentation and have a more indolent evolution.
We present the case of a 50-years-old woman with an unplanned skin EHE resection. She presented a relapse on the previous scar and a mammary gland metastasis. Both lesions were successfully removed and follow-up was decided. To our knowledge this is the first report of a breast metastasis.
There is no solid prospective evidence for the selection of the systemic treatment in case of unresectability and the recommendation based on retrospective studies is antiangiogenic therapy like pazopanib.