Teaching NeuroImages: Gerstmann Syndrome in a Pediatric Patient with a Dominant Parietal Pleomorphic Xanthroastrocytoma
Chattip Prueksapraopong1, Angeline Zhou1, Bryant Yu1, Carrie Ip1, Audrey Nath2*
1University of Hawaii, Honolulu, HI, USA
2University of Texas Medical Branch, Galveston, TX, USA
*Corresponding Author: Audrey Nath, University of Texas Medical Branch, Galveston, TX, USA.
Received: 15 May 2023; Accepted: 30 May 2023; Published: 12 June 2023
Citation: Chattip Prueksapraopong, Angeline Zhou, Bryant Yu, Carrie Ip, Audrey Nath. Teaching NeuroImages: Gerstmann Syndrome in a Pediatric Patient with a Dominant Parietal Pleomorphic Xanthroastrocytoma. Archives of Clinical and Medical Case Reports. 7 (2023): 269-270.View / Download Pdf Share at Facebook
Gerstmann Syndrome; NeuroImages
MRI showing the 5.8 x 5.8 x 5.2 cm calcified mass in the left frontoparietal region, causing mild mass effect on the left lateral ventricle, on axial T2 FLAIR (A) and coronal T2- weighted (B) sequences.
A 13-year-old right-handed girl presented with a 2 year history of worsening headaches and 1 year history of focal seizures. Her mother also reported new difficulties in math class at school, as well as worsening handwriting. On examination, when asked to show her raise her left thumb, she raised her right thumb. She was unable to perform serial 7’s, and when asked to write her name, her handwriting was unreadable. Brain MRI was significant for a large left frontoparietal calcified mass. Pathology revealed a diagnosis of pleomorphic xanthoastrocytoma.
The patient’s left-right confusion, acalculia and agraphia appear consistent with a partial Gerstmann syndrome , seen with dominant parietal lesions and may be seen as an ictal phenomenon .
Chattip Prueksapraopong: Drafting/revision of the manuscript for content, including medical writing for content; Major role in the acquisition of data
Angeline Zhou: Major role in the acquisition of data Bryant Yu: Major role in the acquisition of data Carrie Ip: Major role in the acquisition of data
Audrey Nath: Drafting/revision of the manuscript for content, including medical writing for content; Major role in the acquisition of data; Analysis or interpretation of data
The authors report no targeted funding.
C. Prueksapraopong, A. Zhou, B. Yu, C. Ip and A. Nath all report no disclosures.
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